1Department of Plastic Surgery, College of Medicine, The Catholic University of Korea, Gyeonggi, Korea. yjkim@hfh.cuk.ac.kr 2Department of Pathology, College of Medicine, The Catholic University of Korea, Gyeonggi, Korea.
Abstract
PURPOSE Malignant peripheral nerve sheath tumors (MPNSTs) are rare neoplasms, usually arising from somatic soft tissues or peripheral nerves. Primary MPNST of the scalp is extremely rare. The case is being reported for its rarity. METHODS: A 53-year-old female was presented with a scalp mass on vertex area. The tumor was localized in scalp skin and did not invade underlying periosteum or skull and treated with complete surgical excision followed by adjuvant chemotherapy and radiotherapy. RESULTS Histologically, the tumor showed malignant spindle cells with focal S-100 positivity on immunohistochemistry and a diagnosis of MPNST was made. CONCLUSION Authors experienced a rare case of primary scalp MPNST and report the case.